GAA

Aliases: LYAG
Other: lysosomal alpha-glucosidase|acid maltase|aglucosidase alfa|glucosidase alpha, acid

This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with ... see more

Purified


Popular GAA Purified Antibodies


Company /
SKU
Applications Marker /
Reactivity
Host / Isotype /
Clone
Size /
Price
Details
Biorbyt
GAA-200ug
ELISA,ICC,IF,IHC-P GAA
Human,Mouse,Rat
Rabbit
IgG
200 μg
$610
Details 
LifeSpan
LS-C197260
ELISA,WB GAA
Human
Mouse
IgG1
3C6
100 μg
$444
Details 
Aviva Systems Biology
OAAN02361
WB,IHC,IP GAA
Human,Mouse,Rat
Rabbit
IgG
50 μl
$130
Details 
Biorbyt
orb647957
IF,IP,WB GAA
Human,Mouse,Rat
Rabbit
IgG
100 μl
$680
Details 
Biorbyt
orb41825-50ug
ELISA,WB,IHC-P,IF,ICC GAA
Human
Rabbit
IgG
50 μg
$250
Details 
LifeSpan
LS-C665705
ELISA,IHC,IP,WB GAA
Mouse,Rat,Human
Rabbit
IgG
100 μg
Details 
OriGene
AP51752PU-N
IHC,WB GAA
Human
Rabbit
IgG
400 μl
$330
Details 
Biorbyt
orb636727
IHC-P,WB GAA
Human
Mouse
IgG1
43G7
100 μl
$726
Details 
Biorbyt
GAA-200ul
IP,WB GAA
Human,Mouse,Rat
Rabbit
IgG
200 μl
$502
Details 
Biorbyt
orb627174
ELISA,IHC-P,IP,WB GAA
Human,Mouse,Rat
Rabbit
IgG
100 ug
$452
Details 
OriGene
TA334653
WB GAA
Human,Canine,Porcine,Guinea Pig,Rat,Mouse,Bovine,H
Rabbit
IgG
50 μg
$360
Details 
St John's Laboratory
STJ29987-100μl
WB GAA
Human,Mouse,Rat
Rabbit
IgG
100 μl
$357
Details 
Elabscience
E-AB-65554-200UL
WB GAA
Human,Mouse,Rat
Rabbit
IgG
200 μl
$481
Details 
Bioss
bs-13254R
ELISA,IHC-P,IHC-Fr,IF,ICC GAA
Mouse
Rabbit
IgG
100 μl
$375
Details 
Aviva Systems Biology
OACD03674
WB,ICC,IHC-P,IHC-Fr,ELISA GAA
Rat
Rabbit
IgG
100 μg
$330
Details 
Atlas Antibodies
HPA026970
IHC,WB GAA
Human
Rabbit
IgG
Polyclonal
100 μl
$439
Details 
Biorbyt
orb579131
WB GAA
Human
Rabbit
IgG
100 ul
$527
Details 
Boster Biological Technology
A01548-1
IHC,WB GAA
Human,Mouse,Rat
Rabbit
IgG
100 μl
$299
Details 
Aviva Systems Biology
OACD03676
WB,ICC,IHC-P,IHC-Fr,ELISA GAA
Human
Rabbit
IgG
100 μg
$305
Details 
Biorbyt
orb155646
ELISA,ICC,IF,IHC-P GAA
Human,Mouse,Rat
Rabbit
IgG
200 μg
$610
Details 
Biorbyt
orb314347-200ul
WB,IHC-P GAA
Human
Rabbit
IgG
200 μl
$672
Details 
Biorbyt
orb41825-20ug(TrialSize)
ELISA,WB,IHC-P,IF,ICC GAA
Human
Rabbit
IgG
20 μg
$85
Details 
Aviva Systems Biology
OACD03678
WB,ICC,IHC-P,IHC-Fr,ELISA GAA
Mouse
Rabbit
IgG
100 μg
$310
Details 
LifeSpan
LS-B10678
IHC,IHC-P,WB GAA
Human
Rabbit
IgG
200 μl
$532
Details 
Biorbyt
orb20696
Dot Blot,IEP GAA
Yeast
Rabbit
IgG
1 mg
$673
Details 
ProSci
56-495-400UL
WB,IHC-P,IHC GAA
Human
Rabbit
Ig
400 μl
$482
Details 
Novus Biologicals
H00002548-D01P
WB GAA
Human,Mouse
Rabbit
IgG
100 μg
$429
Details 
Boster Biological Technology
A01548-2
GAA
Human,Mouse,Rat
Rabbit
IgG
100 μl
$299
Details 
R&D Systems
MAB83291-SP
WB,IHC GAA
Human
Rabbit
IgG
2489B
25 μg
$129
Details 
LifeSpan
LS-C310421
WB GAA
Mouse,Human
Rabbit
IgG
100 μg
Details 
Aviva Systems Biology
OACD03673
WB,ICC,IHC-P,IHC-Fr,ELISA GAA
Human
Rabbit
IgG
100 μg
$305
Details 
R&D Systems
MAB8329-SP
WB,IHC GAA
Human
Rabbit
IgG
2489C
25 μg
$129
Details 
Novus Biologicals
NBP1-69295
WB,IHC,ICC, IF,IHC-P GAA
Human
Rabbit
IgG
100 ul
$377
Details 
LifeSpan
LS-C80648
WB GAA
Zebrafish,Porcine,Rat,Hamster,Mouse,Canine,Guinea Pig,Bovine,Human,Monkey
Rabbit
IgG
100 μl
Details 
Biorbyt
orb155646-100ug
ELISA,ICC,IF,IHC-P GAA
Human,Mouse,Rat
Rabbit
IgG
100 μg
$386
Details 
Aviva Systems Biology
OALA06663
IHC-P,WB GAA
Human
Mouse
IgG1
43G7
100 μl
$395
Details 
Novus Biologicals
NBP1-69295-20ul
WB,IHC,ICC, IF,IHC-P GAA
Human
Rabbit
IgG
20 ul
$140
Details 
Biorbyt
orb389407-100ug
WB,IHC-P GAA
Human,Rat
Rabbit
IgG
100 μg
$553
Details 
Biorbyt
orb41825-100ug
ELISA,WB,IHC-P,IF,ICC GAA
Human
Rabbit
IgG
100 μg
$415
Details 
Novus Biologicals
H00002548-B01P
WB GAA
Human
Mouse
IgG
0.05 mg
$464
Details 
St John's Laboratory
STJ29987-50μl
WB GAA
Human,Mouse,Rat
Rabbit
IgG
50 μl
$248
Details 
Novus Biologicals
NBP2-48576-25ul
WB,IHC,IHC-P GAA
Human
Rabbit
IgG
25ul
$209
Details 
Biorbyt
orb20870
Dot Blot,IEP GAA
Yeast
Rabbit
IgG
10 mg
$413
Details 
Biorbyt
orb183805-100ug
WB,IHC-P,ELISA GAA
Human,Mouse,Rat
Rabbit
IgG
100 μg
$366
Details 
Atlas Antibodies
HPA029126
IHC,WB GAA
Human
Rabbit
IgG
Polyclonal
100 μl
$439
Details 
Aviva Systems Biology
OAGA03478
ICC,IF,IHC-P,WB GAA
Human
Rabbit
IgG
100 μl
$319
Details 
Aviva Systems Biology
OACD03675
WB,ICC,IHC-P,IHC-Fr,ELISA GAA
Mouse
Rabbit
IgG
100 μg
$310
Details 
Biorbyt
orb30560-400ul
ELISA,WB,IHC-P GAA
Human
Rabbit
IgG
400 μl
$383
Details 
Biorbyt
GAA-100ul
IP,WB GAA
Human,Mouse,Rat
Rabbit
IgG
100 μl
$320
Details 
Aviva Systems Biology
OACD03677
WB,ICC,IHC-P,IHC-Fr,ELISA GAA
Rat
Rabbit
IgG
100 μg
$330
Details 
 Browse 34 more GAA / Purified antibodies.