GAA
Aliases: | LYAG |
---|---|
Other: | lysosomal alpha-glucosidase|acid maltase|aglucosidase alfa|glucosidase alpha, acid |
This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with ... see more
Purified
Popular GAA Purified Antibodies
Company / SKU |
Applications | Marker / Reactivity |
Host / Isotype / Clone |
Size / Price |
Details | |
---|---|---|---|---|---|---|
Biorbyt GAA-200ug |
ELISA,ICC,IF,IHC-P | GAA Human,Mouse,Rat |
Rabbit IgG |
200 μg $610 |
Details | |
LifeSpan LS-C197260 |
ELISA,WB | GAA Human |
Mouse IgG1 3C6 |
100 μg $444 |
Details | |
Aviva Systems Biology OAAN02361 |
WB,IHC,IP | GAA Human,Mouse,Rat |
Rabbit IgG |
50 μl $130 |
Details | |
Biorbyt orb647957 |
IF,IP,WB | GAA Human,Mouse,Rat |
Rabbit IgG |
100 μl $680 |
Details | |
Biorbyt orb41825-50ug |
ELISA,WB,IHC-P,IF,ICC | GAA Human |
Rabbit IgG |
50 μg $250 |
Details | |
LifeSpan LS-C665705 |
ELISA,IHC,IP,WB | GAA Mouse,Rat,Human |
Rabbit IgG |
100 μg |
Details | |
OriGene AP51752PU-N |
IHC,WB | GAA Human |
Rabbit IgG |
400 μl $330 |
Details | |
Biorbyt orb636727 |
IHC-P,WB | GAA Human |
Mouse IgG1 43G7 |
100 μl $726 |
Details | |
Biorbyt GAA-200ul |
IP,WB | GAA Human,Mouse,Rat |
Rabbit IgG |
200 μl $502 |
Details | |
Biorbyt orb627174 |
ELISA,IHC-P,IP,WB | GAA Human,Mouse,Rat |
Rabbit IgG |
100 ug $452 |
Details | |
OriGene TA334653 |
WB | GAA Human,Canine,Porcine,Guinea Pig,Rat,Mouse,Bovine,H |
Rabbit IgG |
50 μg $360 |
Details | |
St John's Laboratory STJ29987-100μl |
WB | GAA Human,Mouse,Rat |
Rabbit IgG |
100 μl $357 |
Details | |
Elabscience E-AB-65554-200UL |
WB | GAA Human,Mouse,Rat |
Rabbit IgG |
200 μl $481 |
Details | |
Bioss bs-13254R |
ELISA,IHC-P,IHC-Fr,IF,ICC | GAA Mouse |
Rabbit IgG |
100 μl $375 |
Details | |
Aviva Systems Biology OACD03674 |
WB,ICC,IHC-P,IHC-Fr,ELISA | GAA Rat |
Rabbit IgG |
100 μg $330 |
Details | |
Atlas Antibodies HPA026970 |
IHC,WB | GAA Human |
Rabbit IgG Polyclonal |
100 μl $439 |
Details | |
Biorbyt orb579131 |
WB | GAA Human |
Rabbit IgG |
100 ul $527 |
Details | |
Boster Biological Technology A01548-1 |
IHC,WB | GAA Human,Mouse,Rat |
Rabbit IgG |
100 μl $299 |
Details | |
Aviva Systems Biology OACD03676 |
WB,ICC,IHC-P,IHC-Fr,ELISA | GAA Human |
Rabbit IgG |
100 μg $305 |
Details | |
Biorbyt orb155646 |
ELISA,ICC,IF,IHC-P | GAA Human,Mouse,Rat |
Rabbit IgG |
200 μg $610 |
Details | |
Biorbyt orb314347-200ul |
WB,IHC-P | GAA Human |
Rabbit IgG |
200 μl $672 |
Details | |
Biorbyt orb41825-20ug(TrialSize) |
ELISA,WB,IHC-P,IF,ICC | GAA Human |
Rabbit IgG |
20 μg $85 |
Details | |
Aviva Systems Biology OACD03678 |
WB,ICC,IHC-P,IHC-Fr,ELISA | GAA Mouse |
Rabbit IgG |
100 μg $310 |
Details | |
LifeSpan LS-B10678 |
IHC,IHC-P,WB | GAA Human |
Rabbit IgG |
200 μl $532 |
Details | |
Biorbyt orb20696 |
Dot Blot,IEP | GAA Yeast |
Rabbit IgG |
1 mg $673 |
Details | |
ProSci 56-495-400UL |
WB,IHC-P,IHC | GAA Human |
Rabbit Ig |
400 μl $482 |
Details | |
Novus Biologicals H00002548-D01P |
WB | GAA Human,Mouse |
Rabbit IgG |
100 μg $429 |
Details | |
Boster Biological Technology A01548-2 |
GAA Human,Mouse,Rat |
Rabbit IgG |
100 μl $299 |
Details | ||
R&D Systems MAB83291-SP |
WB,IHC | GAA Human |
Rabbit IgG 2489B |
25 μg $129 |
Details | |
LifeSpan LS-C310421 |
WB | GAA Mouse,Human |
Rabbit IgG |
100 μg |
Details | |
Aviva Systems Biology OACD03673 |
WB,ICC,IHC-P,IHC-Fr,ELISA | GAA Human |
Rabbit IgG |
100 μg $305 |
Details | |
R&D Systems MAB8329-SP |
WB,IHC | GAA Human |
Rabbit IgG 2489C |
25 μg $129 |
Details | |
Novus Biologicals NBP1-69295 |
WB,IHC,ICC, IF,IHC-P | GAA Human |
Rabbit IgG |
100 ul $377 |
Details | |
LifeSpan LS-C80648 |
WB | GAA Zebrafish,Porcine,Rat,Hamster,Mouse,Canine,Guinea Pig,Bovine,Human,Monkey |
Rabbit IgG |
100 μl |
Details | |
Biorbyt orb155646-100ug |
ELISA,ICC,IF,IHC-P | GAA Human,Mouse,Rat |
Rabbit IgG |
100 μg $386 |
Details | |
Aviva Systems Biology OALA06663 |
IHC-P,WB | GAA Human |
Mouse IgG1 43G7 |
100 μl $395 |
Details | |
Novus Biologicals NBP1-69295-20ul |
WB,IHC,ICC, IF,IHC-P | GAA Human |
Rabbit IgG |
20 ul $140 |
Details | |
Biorbyt orb389407-100ug |
WB,IHC-P | GAA Human,Rat |
Rabbit IgG |
100 μg $553 |
Details | |
Biorbyt orb41825-100ug |
ELISA,WB,IHC-P,IF,ICC | GAA Human |
Rabbit IgG |
100 μg $415 |
Details | |
Novus Biologicals H00002548-B01P |
WB | GAA Human |
Mouse IgG |
0.05 mg $464 |
Details | |
St John's Laboratory STJ29987-50μl |
WB | GAA Human,Mouse,Rat |
Rabbit IgG |
50 μl $248 |
Details | |
Novus Biologicals NBP2-48576-25ul |
WB,IHC,IHC-P | GAA Human |
Rabbit IgG |
25ul $209 |
Details | |
Biorbyt orb20870 |
Dot Blot,IEP | GAA Yeast |
Rabbit IgG |
10 mg $413 |
Details | |
Biorbyt orb183805-100ug |
WB,IHC-P,ELISA | GAA Human,Mouse,Rat |
Rabbit IgG |
100 μg $366 |
Details | |
Atlas Antibodies HPA029126 |
IHC,WB | GAA Human |
Rabbit IgG Polyclonal |
100 μl $439 |
Details | |
Aviva Systems Biology OAGA03478 |
ICC,IF,IHC-P,WB | GAA Human |
Rabbit IgG |
100 μl $319 |
Details | |
Aviva Systems Biology OACD03675 |
WB,ICC,IHC-P,IHC-Fr,ELISA | GAA Mouse |
Rabbit IgG |
100 μg $310 |
Details | |
Biorbyt orb30560-400ul |
ELISA,WB,IHC-P | GAA Human |
Rabbit IgG |
400 μl $383 |
Details | |
Biorbyt GAA-100ul |
IP,WB | GAA Human,Mouse,Rat |
Rabbit IgG |
100 μl $320 |
Details | |
Aviva Systems Biology OACD03677 |
WB,ICC,IHC-P,IHC-Fr,ELISA | GAA Rat |
Rabbit IgG |
100 μg $330 |
Details | |
Browse 34 more GAA / Purified antibodies. |