BCKDHB

Aliases: BCKDE1B, BCKDH E1-beta, E1B
Other: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial|E1b-beta subunit of the branched-chain complex|branched chain alpha-ketoacid dehydrogenase E1-beta subunit|branched chain keto acid dehydrogenase E1, beta polypeptide|branched-chain alpha-keto acid dehydrogenase E1 component beta chain|testis secretory sperm-binding protein Li 240mP

This gene encodes the E1 beta subunit of branched-chain keto acid dehydrogenase, which is a multienzyme complex associated with the inner membrane of mitochondria. This enzyme complex functions in the catabolism of branched-chain amino acids. Mutations in this gene have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in ... see more

Purified


Popular BCKDHB Purified Antibodies


Company /
SKU
Applications Marker /
Reactivity
Host / Isotype /
Clone
Size /
Price
Details
Biorbyt
orb28590-400ul
ELISA,WB,IHC-P,IF,ICC,FC BCKDHB
Human
Rabbit
IgG
400 μl
$383
Details 
Aviva Systems Biology
ARP58593_P050
WB BCKDHB
Bovine,Canine,Equine,Human,Porcine,Rabbit,Rat
Rabbit
IgG
100 μl
$289
Details 
LifeSpan
LS-C156767
FC,IF,IHC,IHC-P,WB BCKDHB
Human
Rabbit
IgG
400 μl
$407
Details 
Biorbyt
orb625079
ELISA,IHC-P,WB BCKDHB
Human,Mouse,Rat
Rabbit
IgG
100 ug
$452
Details 
OriGene
TA344275
WB BCKDHB
Human
Rabbit
IgG
50 μg
$360
Details 
OriGene
TA324362
FC,WB,IF BCKDHB
Human
Rabbit
IgG
400 μl
$410
Details 
Abbexa
abx230834
ELISA,WB,IHC BCKDHB
Human,Mouse,Rat
Rabbit
IgG
100 μg
$434
Details 
Atlas Antibodies
HPA031580
IHC,WB BCKDHB
Human
Rabbit
IgG
Polyclonal
100 μl
$439
Details 
Novus Biologicals
NBP3-17345-100ul
ICC,IF BCKDHB
Human
Rabbit
IgG
100 μl
$449
Details 
Novus Biologicals
NBP2-92027-0.02ml
WB BCKDHB
Mouse
Rabbit
IgG
0.02 ml
$151
Details 
LifeSpan
LS-C319798
ELISA,FC,IF,IHC,WB BCKDHB
Human
Rabbit
IgG
200 μl
Details 
Thermo Fisher Scientific
PA5-24166
WB,FC,IF,IHC,IHC-P BCKDHB
Human
Rabbit
IgG
400 μl
$330
Details 
Biorbyt
orb28590
ELISA,FC,ICC,IF,IHC-P,WB BCKDHB
Human
Rabbit
IgG
400 ul
$626
Details 
Novus Biologicals
NBP2-92027-0.1ml
WB BCKDHB
Mouse
Rabbit
IgG
0.1 ml
$356
Details 
LifeSpan
LS-C201719
WB BCKDHB
Human,Monkey
Rabbit
IgG
100 μl
$482
Details 
Biorbyt
orb615402-50ul
WB BCKDHB
Mouse
Rabbit
IgG
50 μl
$308
Details 
Novus Biologicals
NBP2-92027-20ul
WB BCKDHB
Mouse
Rabbit
IgG
20 μl
$179
Details 
LifeSpan
LS-C659432
ELISA,IHC,WB BCKDHB
Human
Rabbit
IgG
100 μg
Details 
St John's Laboratory
STJ112553-50μl
WB BCKDHB
Mouse
Rabbit
IgG
50 μl
$248
Details 
Boster Biological Technology
A05595
WB BCKDHB
Human,Rat
Rabbit
IgG
100 μl
$299
Details 
Novus Biologicals
NBP3-17345-25ul
ICC,IF BCKDHB
Human
Rabbit
IgG
25 μl
$199
Details 
Novus Biologicals
NBP2-29984
FC,IHC-P,WB,ICC, IF,IHC BCKDHB
Human
Rabbit
IgG
RB20925
400 μl
$379
Details 
Biorbyt
orb537748-50ul
WB BCKDHB
Mouse
Rabbit
IgG
50 μl
$315
Details 
ProSci
55-327-400UL
WB,IHC-P,IF,FC BCKDHB
Human
Rabbit
Ig
400 μl
$482
Details 
Novus Biologicals
NBP1-86326
WB,IHC,IHC-P BCKDHB
Human
Rabbit
IgG
0.1 ml
$472
Details 
Aviva Systems Biology
OAAB00689
WB,IHC-P,IF,FC BCKDHB
Human
Rabbit
Ig
400 μl
$320
Details 
Biorbyt
orb615402-100ul
WB BCKDHB
Mouse
Rabbit
IgG
100 μl
$561
Details 
Biorbyt
orb258591
ELISA,IHC-P,WB BCKDHB
Human
Rabbit
IgG
100 ug
$425
Details 
Biorbyt
orb818532
ELISA,WB BCKDHB
Bovine
Rabbit
IgG
10 mg
$49,660
Details 
Biorbyt
orb584052
WB BCKDHB
Animal,Bovine,Canine,Human,Porcine,Rat
Rabbit
IgG
100 ul
$527
Details 
Novus Biologicals
NBP2-92027-100ul
WB BCKDHB
Mouse
Rabbit
IgG
100 μl
$399
Details 
St John's Laboratory
STJ112553-100μl
WB BCKDHB
Mouse
Rabbit
IgG
100 μl
$357
Details 
Biorbyt
orb537748-200ul
WB BCKDHB
Mouse
Rabbit
IgG
200 μl
$604
Details 
Novus Biologicals
NBP2-84500-0.1ml
WB BCKDHB
Human
Rabbit
IgG
0.1ml
$356
Details 
St John's Laboratory
STJ111483-100μl
WB,IHC,IF,FC BCKDHB
Human
Rabbit
IgG
100 μl
$357
Details 
Thermo Fisher Scientific
PA524166
WB,IF,FC BCKDHB
Human
Rabbit
IgG
Polyclonal
400 μl
$324
Details 
Biorbyt
orb537748-100ul
WB BCKDHB
Mouse
Rabbit
IgG
100 μl
$384
Details 
Biorbyt
orb258591-100ug
ELISA,WB,IHC-P BCKDHB
Human
Rabbit
IgG
100 μg
$425
Details 
 Browse BCKDHB / Purified antibodies.